Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Victorian Clinical Genetics Services, |
RCV001089969 | SCV001244972 | pathogenic | Arterial calcification, generalized, of infancy, 2 | 2018-04-19 | criteria provided, single submitter | clinical testing | This sample showed a female molecular karyotype with an interstitial deletion of approximately 12 kiloabases on the short arm of one chromosome 16 at cytogenetic band p13.11. This heterozygous microdeletion involves exons 23-28 of the ABCC6 gene. Homozygous and compound heterozygous variants and deletions of this gene are associated with Generalized Arterial Calcification of Infancy (GACI GeneReviews PMID: 25392903). |