Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Clinical Genetics Unit, |
RCV002463571 | SCV002605167 | pathogenic | Werner syndrome | 2022-11-13 | no assertion criteria provided | clinical testing | The patient has all clinical features of Werner Syndrome: short tall, gray hair and alopecia from her twenties, early cataracts, skin atrophy, sclerodermic changes, calcinosis cutis, torpid ulcers on lower limbs, diabetes mellitus, lipodystrophy and advanced osteoporosis. The patient has this variant on homocigosis. Her parents didn't know being consanguineous, but they were from the same litte village in Spain. |