Total submissions: 1
| Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
|---|---|---|---|---|---|---|---|---|
| Medical Genetics Lab, |
RCV000757957 | SCV000886405 | uncertain significance | Intellectual disability, mild | 2019-02-19 | criteria provided, single submitter | clinical testing | This is a very rare, de novo CNV. The proximal break point involves ANKRD11, but the phenotype of the patient is not strongly suggestive for KBG syndrome. Furthermore, this patient carries a second de novo CNV (dup1q21.1), which is known to cause intellectual disability with variable clinical expressivity and incomplete penetrance, and may explain (at least in part) the phenotype of this patient. |