Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV004583977 | SCV005065091 | uncertain significance | Congenital myopathy 4B, autosomal recessive; Congenital myopathy with fiber type disproportion | 2020-02-21 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This variant has not been reported in the literature in individuals with TPM3-related conditions. This variant is a sub-genic deletion of the genomic region encompassing exons 3-9 of the TPM3 gene. While this deletion is not anticipated to result in nonsense mediated decay, it is expected to create a truncated protein product. |