Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV004584053 | SCV005066446 | pathogenic | Granulomatous disease, chronic, autosomal recessive, cytochrome b-positive, type 2 | 2023-11-14 | criteria provided, single submitter | clinical testing | This variant results in the deletion of exons 1-13 and part of exon 14 (c.-27208_1339delins51) of the NCF2 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in NCF2 are known to be pathogenic (PMID: 10498624, 20167518). This variant has not been reported in the literature in individuals affected with NCF2-related conditions. For these reasons, this variant has been classified as Pathogenic. |