Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001962996 | SCV002232104 | pathogenic | Familial adenomatous polyposis 2 | 2021-02-23 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. The region of the MUTYH gene that includes exon(s) 15-16 has been determined to be clinically significant (PMID: 16557584, 17949294, 19806110, 25820570). Therefore, deletions that encompass that region are likely to disrupt protein function and cause disease. This variant has not been reported in the literature in individuals with MUTYH-related conditions. This variant results in the deletion of exon(s) 10-16 and part of exon 9 (c.740_*1527del) of the MUTYH gene. While this deletion is not anticipated to lead to nonsense mediated decay, it is expected to alter mRNA translation or result in a truncated protein product. |