Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV004584107 | SCV005066501 | uncertain significance | Immunodeficiency 14 | 2023-09-11 | criteria provided, single submitter | clinical testing | This variant results in the deletion of exons 10-15 and part of exon 16 (c.1243-285_2054) of the PIK3CD gene. It is expected to disrupt RNA splicing. Variants that disrupt the donor or acceptor splice site typically lead to a loss of protein function (PMID: 16199547), however the current clinical and genetic evidence is not sufficient to establish whether loss-of-function variants in PIK3CD cause disease. This variant has not been reported in the literature in individuals affected with PIK3CD-related conditions. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. |