Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001032495 | SCV001195802 | pathogenic | Senior-Loken syndrome 7; Bardet-Biedl syndrome 16 | 2019-10-14 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant is an out-of-frame deletion of the genomic region encompassing exons 14 of the SDCCAG8 gene. This is expected to create a premature translational stop signal and result in an absent or disrupted protein product. This variant has not been reported in the literature in individuals with SDCCAG8-related conditions. Loss-of-function variants in SDCCAG8 are known to be pathogenic (PMID: 20835237). |