Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV004582558 | SCV005063174 | likely pathogenic | Nemaline myopathy 2 | 2023-06-16 | criteria provided, single submitter | clinical testing | This variant has not been reported in the literature in individuals affected with NEB-related conditions. This variant results in the deletion of exon 64 and part of exon 65 (c.8995-1051_9294del) of the NEB gene. It is expected to disrupt RNA splicing. Variants that disrupt the donor or acceptor splice site typically lead to a loss of protein function (PMID: 16199547), and loss-of-function variants in NEB are known to be pathogenic (PMID: 25205138). In summary, the currently available evidence indicates that the variant is pathogenic, but additional data are needed to prove that conclusively. Therefore, this variant has been classified as Likely Pathogenic. |