Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001910619 | SCV002191324 | pathogenic | Primary pulmonary hypertension | 2021-08-12 | criteria provided, single submitter | clinical testing | This variant is a gross deletion of the genomic region encompassing exon(s) 10 of the BMPR2 gene. This deletion is out-of-frame, and is expected to create a premature termination codon and result in an absent or disrupted protein product. Loss-of-function variants in BMPR2 are known to be pathogenic (PMID: 16429395). A similar copy number variant has been observed in individuals with pulmonary arterial hypertension (PMID: 16429403, 23579436). For these reasons, this variant has been classified as Pathogenic. |