Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001963049 | SCV002243967 | pathogenic | Cholestanol storage disease | 2023-07-07 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant has not been reported in the literature in individuals affected with CYP27A1-related conditions. A gross deletion of the genomic region encompassing the full coding sequence of the CYP27A1 gene has been identified. Loss-of-function variants in CYP27A1 are known to be pathogenic (PMID: 9392430, 10775536, 26937392). The boundaries of this event are unknown as they extend beyond the assayed region for this gene and therefore may encompass additional genes. |