Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001033955 | SCV001197263 | pathogenic | Pulmonary hypertension, primary, 1 | 2019-12-02 | criteria provided, single submitter | clinical testing | This variant is an out-of-frame deletion of the genomic region encompassing exon 5 of the BMPR2 gene. This is expected to create a premature translational stop signal and result in an absent or disrupted protein product. A similar deletion of exon 5 has been reported in an individual referred for genetic testing for pulmonary arterial hypertension (PMID: 26387786). Loss-of-function variants in BMPR2 are known to be pathogenic (PMID: 16429395). For these reasons, this variant has been classified as Pathogenic. |
Labcorp Genetics |
RCV001383552 | SCV001582718 | pathogenic | Primary pulmonary hypertension | 2019-11-25 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. Loss-of-function variants in BMPR2 are known to be pathogenic (PMID: 16429395). A similar deletion of exon 5 has been reported in an individual referred for genetic testing for pulmonary arterial hypertension (PMID: 26387786). This variant is an out-of-frame deletion of the genomic region encompassing exon 5 of the BMPR2 gene. This is expected to create a premature translational stop signal and result in an absent or disrupted protein product. |