Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Invitae | RCV001876459 | SCV002119735 | pathogenic | Cerebral cavernous malformation 2 | 2023-11-03 | criteria provided, single submitter | clinical testing | This variant is a gross deletion of the genomic region encompassing exon(s) 6 of the CCM2 gene. This deletion is out-of-frame, and is expected to create a premature termination codon and result in an absent or disrupted protein product. Loss-of-function variants in CCM2 are known to be pathogenic (PMID: 18300272, 24689081). A similar copy number variant has been observed in individual(s) with clinical features of cerebral cavernous malformations (PMID: 23595507). For these reasons, this variant has been classified as Pathogenic. |