Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Undiagnosed Diseases Network, |
RCV001269480 | SCV001449494 | pathogenic | Kleefstra syndrome 1 | 2020-10-13 | criteria provided, single submitter | clinical testing | 16,119bp tandem duplication involving exons 5 and 6. Results in frameshift and introduction of termination codon. Paternal mosaicism confirmed in unaffected father. |