Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001390741 | SCV001592552 | pathogenic | PTEN hamartoma tumor syndrome | 2020-05-21 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. While deletion of exons 4-5 has not been reported in the literature, loss-of-function variants in PTEN are known to be pathogenic (PMID: 9467011, 21194675). This variant is an out-of-frame deletion of the genomic region encompassing exons 4-5 of the PTEN gene. This creates a premature translational stop signal and is expected to result in an absent or disrupted protein product. |