Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000558494 | SCV000654984 | uncertain significance | Infantile spasms | 2020-01-27 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. This duplication has not been reported in the literature in individuals with PIK3AP1-related disease. This variant is a gross duplication of the genomic region encompassing most of exon 8 of the PIK3AP1 gene, including the exon 8-intron 8 boundary (c.1267_1375+5394dup). The duplicated copy of this region is in tandem and the effect of this variant on RNA splicing and protein translation is unknown. |