Total submissions: 5
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Laboratory for Molecular Medicine, |
RCV000151031 | SCV000198767 | risk factor | Interstitial lung disease 2 | 2020-03-04 | criteria provided, single submitter | clinical testing | MUC5B c.-3133G>T has been associated with increased risk for idiopathic pulmonary fibrosis. This variant has been observed in multiple ethnic backgrounds with highest frequencies in individuals of Ashkenazi Jewish ancestry (16.2%, Genome Aggregation Database (gnomAD); rs35705950) and is present in ClinVar (ID: 30126). Several studies have reported an odds ratios between 3.7-8.3 for developing pulmonary fibrosis in heterozygous individuals (OR=6.3 [95% CI 4.6-8.7] Borie 2013, OR=6.3 [95% CI 3.1-12.7] Hunninghake 2013, OR=8.3 [95% CI 5.8-11.9] Seibold 2013, OR=4.9 [95% CI 3.42-7.03] Stock 2013, OR=5.72 [95% CI 4.7-7.1] Lee 2015, OR=6.2 [95% CI 5.14-7.48] Zhu 2015) and odds ratios between 11.3-21.7 for developing pulmonary fibrosis in homozygous individuals (OR=21.7 [95% CI 104-45.3] Borie 2013, OR=12.98 [95% CI 7.97-21.12] Lee 2015, OR=11.29 [95% CI 5.69-22.40] Zhu 2015). MUC5B c.-3133G>T is a promoter variant that results in increased MUC5B expression (Seibold 2011, Nakano 2016, Kaur 2017). In summary, this variant is an established risk factor for idiopathic pulmonary fibrosis. |
Ce |
RCV002292458 | SCV002585262 | benign | not provided | 2022-08-01 | criteria provided, single submitter | clinical testing | MUC5B: BS1, BS2 |
OMIM | RCV000023036 | SCV000044327 | risk factor | Pulmonary fibrosis, idiopathic, susceptibility to | 2013-06-06 | no assertion criteria provided | literature only | |
HLA Laboratory, |
RCV002466249 | SCV002546355 | uncertain significance | Susceptibility to coronavirus disease (COVID-19) severity and mortality due to low plasma levels of MUC5B | 2022-05-13 | no assertion criteria provided | research | Differences in plasma levels of MUC5B according to genotypes |
HLA Laboratory, |
RCV004794344 | SCV005045620 | association | Antisynthetase syndrome | 2024-05-15 | no assertion criteria provided | research | Usual Interstitial Pneumonia was observed in the patients |