Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000707924 | SCV000837034 | pathogenic | Hereditary diffuse gastric adenocarcinoma | 2018-03-12 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant is an out-of-frame deletion of the genomic region encompassing exon 2 of the CDH1 gene. This is expected to create a premature translational stop signal and result in an absent or disrupted protein product. Deletion of exon 2 has not been reported in the literature in individuals with CDH1-related disease. Loss-of-function variants in CDH1 are known to be pathogenic (PMID: 15235021, 20373070). |