Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001033476 | SCV001196783 | pathogenic | Hereditary diffuse gastric adenocarcinoma | 2019-12-30 | criteria provided, single submitter | clinical testing | This variant is an out-of-frame deletion of the genomic region encompassing exon 3 of the CDH1 gene. This is expected to create a premature translational stop signal and result in an absent or disrupted protein product. A deletion of exon 3 has been reported in the literature in a family with gastric cancer (PMID: 21777349). Experimental studies have shown that exon 3 deletion impairs the cell cell adhesion function of CDH1 (PMID: 21777349). Loss-of-function variants in CDH1 are known to be pathogenic (PMID: 15235021, 20373070). For these reasons, this variant has been classified as Pathogenic. |