Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000468288 | SCV000563854 | pathogenic | Hereditary diffuse gastric adenocarcinoma | 2016-07-02 | criteria provided, single submitter | clinical testing | This variant is a gross deletion of the genomic region encompassing exon 3 of the CDH1 gene. This creates a premature translational stop signal and is expected to result in an absent or disrupted protein product. Loss-of-function variants in CDH1 are known to be pathogenic. A deletion of exon 3 has been reported in the literature in a family with gastric cancer (PMID: 21777349). Experimental studies have shown that this exon deletion impairs the cell-cell adhesion function of CDH1 (PMID: 21777349). For these reasons, this variant has been classified as Pathogenic. |