Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Godley laboratory, |
RCV001250777 | SCV001422441 | pathogenic | Pulmonary fibrosis and/or bone marrow failure, Telomere-related, 4 | 2020-05-18 | criteria provided, single submitter | clinical testing | This heterozygous deletion of exons 1-21 of PARN was found in germline in a patient with ILD/UIP and constrictive bronchiolitis diagnosed at age 61. The variant segregates with disease (ILD) in eight family members. The following ACMG/AMP criteria were used: PVS1, PS4_supporting, PM2, PP1_strong. |