Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001972870 | SCV002243206 | pathogenic | Hereditary diffuse gastric adenocarcinoma | 2021-08-22 | criteria provided, single submitter | clinical testing | This variant is a gross deletion of the genomic region encompassing exon(s) 14-15 of the CDH1 gene. While this deletion is not anticipated to lead to nonsense mediated decay, it is expected to disrupt the C-terminus of the protein. A similar copy number variant has been observed in individual(s) with hereditary diffuse gastric cancer syndrome (Invitae). ClinVar contains an entry for this variant (Variation ID: 845399). The region of the CDH1 gene that includes exon(s) 14-16 has been determined to be clinically significant (Invitae). Therefore, deletions that encompass that region are likely to be disease-causing. For these reasons, this variant has been classified as Pathogenic. |