Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV004581206 | SCV005065300 | pathogenic | Familial cancer of breast; Fanconi anemia complementation group J | 2023-10-26 | criteria provided, single submitter | clinical testing | This variant results in the deletion of exons 1-10 and part of exon 11 (c.-46614_1542del) of the BRIP1 gene. It is expected to result in an absent or disrupted protein product. Loss-of-function variants in BRIP1 are known to be pathogenic (PMID: 16116423, 17033622, 21964575). This variant has not been reported in the literature in individuals affected with BRIP1-related conditions. For these reasons, this variant has been classified as Pathogenic. |