Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000545727 | SCV000628339 | pathogenic | Neurofibromatosis, type 1 | 2017-06-16 | criteria provided, single submitter | clinical testing | Loss-of-function variants in NF1 are known to be pathogenic (PMID: 10712197, 23913538). For these reasons, this variant has been classified as Pathogenic. Deletion of exons 36-44 has not been reported in the literature in individuals with an NF1-related disease. This variant is an out-of-frame deletion of the genomic region encompassing exons 36-44 of the NF1 gene. This creates a premature translational stop signal and is expected to result in an absent or disrupted protein product. |