Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001031633 | SCV001194939 | likely pathogenic | Hereditary breast ovarian cancer syndrome | 2019-11-05 | criteria provided, single submitter | clinical testing | This variant results in a copy number gain of the genomic region encompassing exons 12 to 14 of the BRCA1 gene. While the exact position of this variant cannot be determined from this data, sub-genic copy number gains are generally in tandem (PMID: 25640679) and may result in an absent or disrupted protein product. Similar duplications of exons 12-14 have been observed in individual(s) referred for testing of breast cancer predisposition genes (PMID: 30054569). Loss-of-function variants in BRCA1 are known to be pathogenic (PMID: 20104584). In summary, the currently available evidence indicates that the variant is pathogenic, but additional data are needed to prove that conclusively. Therefore, this variant has been classified as Likely Pathogenic. |