Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Center of Excellence in Genomics and Precision Dentistry, |
RCV002255776 | SCV002526663 | pathogenic | Amelogenesis imperfecta type 1G | criteria provided, single submitter | clinical testing | The heterozygous deletion chr17:66530406_66537936del involving exons 8–11 of FAM20A has been reported in a patient with amelogenesis imperfecta (Pt-1) and her unaffected mother (Nitayavardhana 2020). This variant was identified in compound heterozygous with the c.758A>G (p.Tyr253Cys) in FAM20A which was inherited from her unaffected father. |