Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001959164 | SCV002246099 | pathogenic | Arrhythmogenic right ventricular dysplasia 10 | 2020-11-11 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant has not been reported in the literature in individuals with DSG2-related conditions. This variant is a gross deletion of the genomic region encompassing exon(s) 10-12 of the DSG2 gene. This deletion is out-of-frame, and is expected to create a premature translational stop signal and result in an absent or disrupted protein product. Loss-of-function variants in DSG2 are known to be pathogenic (PMID: 23381804, 23911551). |