Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Molecular Genetics Laboratory, |
RCV000625523 | SCV000598634 | likely pathogenic | Visceral myopathy 1 | 2017-08-31 | no assertion criteria provided | research | The entire MYL9 exon 4 is deleted (the last coding exon of this gene). MYL9 is a gene with a crucial role in smooth muscle contraction and is closely related to the genes previously associated with the megacystis-microcolon-hypoperistalsis syndrome - MMIHS (ACTG2, MYH11, LMOD1 and MYLK). Besides, according to different databases (GeneCard - http://www.genecards.org and Expression Atlas - https://www.ebi.ac.uk/gxa/home), tissues like urinary bladder and colon, clearly affected in MMIHS, have a high mRNA and protein expression level of MYL9. |