Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000258048 | SCV000328219 | uncertain significance | Danon disease | 2016-01-06 | criteria provided, single submitter | clinical testing | A gross duplication of the genomic region encompassing the full coding sequence of the DMD gene has been identified. This gross duplication is not present in population databases. A similar DMD whole gene duplication has been reported in the literature in an individual affected with Duchenne muscular dystrophy and mild intelectual disability (PMID: 22796527). In summary, this is a whole gene duplication with uncertain impact on protein function. It has been classified as a Variant of Uncertain Significance. |