Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000638591 | SCV000760123 | pathogenic | Danon disease | 2021-04-08 | criteria provided, single submitter | clinical testing | For these reasons, this variant has been classified as Pathogenic. This variant has been observed in individual(s) with LAMP2-related disease (Invitae). In at least one individual the variant was observed to be de novo. This variant is a gross deletion of the genomic region encompassing exon(s) 4-8 of the LAMP2 gene. This variant would be expected to be in-frame, preserving the integrity of the reading frame. |