Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Diagnostics Services |
RCV003482204 | SCV004227987 | uncertain significance | Mitochondrial disease | 2023-12-27 | criteria provided, single submitter | clinical testing | The m.13345G>A variant is not present in publicly available population databases like 1000 Genomes, mtDB and our in-house exome database. The variant is present in MITOMAP, HelixMtdb and gnomAD v3.1 databases at low frequencies. This variant has been previously observed in individuals affected with LHON [1, 2] and reported to the MITOMAP database. It has not been reported to the ClinVar or OMIM databases in any affected individuals. This variant is present in the MitImpact database. In-silico pathogenicity prediction programs like SIFT4G, PolyPhen-2, CADD, APOGEE1, APOGEE2, Varsome etc predicted this variant to be likely deleterious, however these predictions were not confirmed by published functional studies. |