Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Wong Mito Lab, |
RCV000850715 | SCV000992948 | benign | Juvenile myopathy, encephalopathy, lactic acidosis AND stroke | 2019-07-12 | criteria provided, single submitter | clinical testing | The NC_012920.1:m.4277T>C variant in MT-TI gene is interpreted to be a Benign variant based on the modified ACMG guidelines (unpublished). This variant meets the following evidence codes reported in the guidelines: BS1, BS4, BP4 |
Stanford Center for Inherited Cardiovascular Disease, |
RCV000223876 | SCV000280194 | uncertain significance | not specified | 2011-11-09 | no assertion criteria provided | clinical testing | Note this variant was found in clinical genetic testing performed by one or more labs who may also submit to ClinVar. Thus any internal case data may overlap with the internal case data of other labs. The interpretation reviewed below is that of the Stanford Center for Inherited Cardiovascular Disease. MT-TI m.4277 T>C Given the lack of conservation in that region and lack of reported case data, (reviewed below) we consider this variant a variant of uncertain significance. This variant has been reported previously in one study examining the relationship between mitochondrial tRNA genes and hypertension, however a functional link between this variant and hypertension was not assessed in this study (Maron B et al., 2002). The 4277 position in the MT-TI gene is not highly conserved across species, with several species harboring a cytosine "C" nucleotide at this position. This variant is located in the DHU-loop of MT-TI and it is not predicted to alter the secondary structure of the tRNA-Gly. The variant has not been observed in various control populations of 2704 to 6391 individuals (Mitomap, mtDB, MItoWheel). |
Genome |
RCV001009555 | SCV001169651 | not provided | not provided | no assertion provided | phenotyping only | Variant interpreted as Uncertain significance and reported on 06-08-2017 by GTR ID 1006. Assertions are reported exactly as they appear on the patient provided laboratory report. GenomeConnect facilitates ClinVar submission from the Association for Creatine Deficiencies registry and does not attempt to reinterpret the variant. |