Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Women's Health and Genetics/Laboratory Corporation of America, |
RCV004701153 | SCV005204717 | likely pathogenic | Alzheimer disease 3 | 2024-06-18 | criteria provided, single submitter | clinical testing | Variant summary: PSEN1 c.437T>C (p.Met146Thr) results in a non-conservative amino acid change in the encoded protein sequence. Four of five in-silico tools predict a damaging effect of the variant on protein function. The variant was absent in 251472 control chromosomes. To our knowledge, no occurrence of c.437T>C in individuals affected with Alzheimer Disease, Type 3 and no experimental evidence demonstrating its impact on protein function have been reported. However, multiple variants affecting the same codon (e.g. Met146Ile, Met146Val, Met146Leu) have been reported in affected individuals and have been classified as pathogenic in ClinVar, indicating the critical relevance of codon 146 to PSEN1 function. No submitters have cited clinical-significance assessments for this variant to ClinVar. Based on the evidence outlined above, the variant was classified as likely pathogenic. |