Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV000640607 | SCV000762201 | uncertain significance | Alzheimer disease 3; Frontotemporal dementia; Pick disease; Acne inversa, familial, 3 | 2017-11-24 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Experimental studies have shown that this missense change reduces the secretase activity of the PSEN1 protein and abrogates production of AB42 and AB40 (PMID: 2793034). This variant has been reported in individuals affected with Alzheimer's disease (PMID: 11524469). ClinVar contains an entry for this variant (Variation ID: 98048). This variant is not present in population databases (ExAC no frequency). This sequence change replaces serine with proline at codon 178 of the PSEN1 protein (p.Ser178Pro). The serine residue is highly conserved and there is a moderate physicochemical difference between serine and proline. |
VIB Department of Molecular Genetics, |
RCV000084334 | SCV000116470 | not provided | not provided | no assertion provided | not provided |