Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Broad Center for Mendelian Genomics, |
RCV003226137 | SCV003922327 | uncertain significance | Autosomal recessive limb-girdle muscular dystrophy type 2D | 2023-05-02 | criteria provided, single submitter | curation | The homozygous c.37+5G>T variant in SGCA was identified by our study in one individual with proximal muscle weakness. The c.37+5G>T variant in SGCA has not been previously reported in individuals with autosomal recessive limb-girdle muscular dystrophy 3. This variant was absent from large population studies. This variant is located in the 5' splice region. Computational tools predict a splicing impact, though this information is not predictive enough to determine pathogenicity. In summary, the clinical significance of the c.37+5G>T variant is uncertain. ACMG/AMP Criteria applied: PM2_Supporting, PM3_Supporting, PP3 (Richards 2015). |