Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Department of Medical Genetics, |
RCV002466746 | SCV002525875 | likely pathogenic | Autosomal recessive limb-girdle muscular dystrophy type 2D | 2022-06-14 | no assertion criteria provided | clinical testing | We investigated an eight years old Moroccan consanguineous male, he presented a proximal progressive symmetric muscle weakness with calf hypertrophy. His serum creatine kinase (CK) level was 20 times increased from normal range. Electromyography (EMG) showed a myogenic pattern in muscles of upper and lower limbs. NGS sequencing identified a novel variant: NM_000023.4(SGCA):c.701delA. This variant has not been previously reported in databases and confirms the diagnosis of a Muscular dystrophy type 2D. It is classified as likely pathogenic on American College of Medical Genetics and Genomics (ACMG) according to these criteria: PVS1 and PM2. |