Total submissions: 9
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000186376 | SCV000486821 | pathogenic | Primary hyperoxaluria, type I | 2016-08-18 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV000186376 | SCV000893592 | pathogenic | Primary hyperoxaluria, type I | 2021-12-25 | criteria provided, single submitter | clinical testing | |
Laboratory of Medical Genetics, |
RCV000186376 | SCV000928385 | pathogenic | Primary hyperoxaluria, type I | 2018-07-27 | criteria provided, single submitter | clinical testing | PS4, PM2, PP4, PP5 |
Invitae | RCV000803735 | SCV000943620 | pathogenic | not provided | 2023-12-28 | criteria provided, single submitter | clinical testing | This sequence change falls in intron 8 of the AGXT gene. It does not directly change the encoded amino acid sequence of the AGXT protein. It affects a nucleotide within the consensus splice site. This variant is present in population databases (rs180177286, gnomAD 0.01%). This variant has been observed in individual(s) with primary hyperoxaluria (PMID: 10862087, 20549407, 22844106, 25363903, 25629080). In at least one individual the data is consistent with being in trans (on the opposite chromosome) from a pathogenic variant. This variant is also known as c.969-3C>G and IVS8-3C>G. ClinVar contains an entry for this variant (Variation ID: 204169). Variants that disrupt the consensus splice site are a relatively common cause of aberrant splicing (PMID: 17576681, 9536098). Algorithms developed to predict the effect of sequence changes on RNA splicing suggest that this variant may disrupt the consensus splice site. For these reasons, this variant has been classified as Pathogenic. |
Ce |
RCV000803735 | SCV002064029 | likely pathogenic | not provided | 2022-02-01 | criteria provided, single submitter | clinical testing | |
Revvity Omics, |
RCV000186376 | SCV003828713 | likely pathogenic | Primary hyperoxaluria, type I | 2022-03-10 | criteria provided, single submitter | clinical testing | |
Baylor Genetics | RCV000186376 | SCV004194238 | pathogenic | Primary hyperoxaluria, type I | 2024-03-26 | criteria provided, single submitter | clinical testing | |
Clinical Biochemistry Laboratory, |
RCV000186376 | SCV000239724 | pathogenic | Primary hyperoxaluria, type I | 2014-11-27 | no assertion criteria provided | research | |
Natera, |
RCV000186376 | SCV001460164 | pathogenic | Primary hyperoxaluria, type I | 2020-09-16 | no assertion criteria provided | clinical testing |