Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV002275738 | SCV002562281 | uncertain significance | not provided | 2022-02-15 | criteria provided, single submitter | clinical testing | Identified in a male with X-ALD who also harbored a second ABCD1 variant (Liu et al., 2022); Not observed at significant frequency in large population cohorts (gnomAD); In silico analysis supports that this missense variant does not alter protein structure/function; This variant is associated with the following publications: (PMID: 34826210) |