Total submissions: 9
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000222854 | SCV000274259 | benign | Hereditary cancer-predisposing syndrome | 2023-01-12 | criteria provided, single submitter | clinical testing | This alteration is classified as benign based on a combination of the following: seen in unaffected individuals, population frequency, intact protein function, lack of segregation with disease, co-occurrence, RNA analysis, in silico models, amino acid conservation, lack of disease association in case-control studies, and/or the mechanism of disease or impacted region is inconsistent with a known cause of pathogenicity. |
Labcorp Genetics |
RCV000144570 | SCV000282700 | likely benign | Familial adenomatous polyposis 1 | 2024-01-19 | criteria provided, single submitter | clinical testing | |
Gene |
RCV000766534 | SCV000569774 | uncertain significance | not provided | 2024-04-08 | criteria provided, single submitter | clinical testing | In silico analysis supports that this missense variant does not alter protein structure/function; Observed in individuals with colorectal cancer (PMID: 28944238); This variant is associated with the following publications: (PMID: 18199528, 28944238, 36243179) |
Color Diagnostics, |
RCV000222854 | SCV000681482 | uncertain significance | Hereditary cancer-predisposing syndrome | 2023-01-24 | criteria provided, single submitter | clinical testing | This missense variant replaces threonine with methionine at codon 562 of the APC protein. Computational prediction suggests that this variant may not impact protein structure and function (internally defined REVEL score threshold <= 0.5, PMID: 27666373). To our knowledge, functional studies have not been reported for this variant. This variant has been reported in an individual affected with colorectal cancer (PMID: 28944238). This variant has been identified in 16/282672 chromosomes in the general population by the Genome Aggregation Database (gnomAD). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
Laboratory for Molecular Medicine, |
RCV000485323 | SCV000731502 | uncertain significance | not specified | 2017-03-20 | criteria provided, single submitter | clinical testing | The p.Thr562Met variant in APC has not been previously reported in individuals w ith familial adenomatous polyposis or other APC-associated disorders but has bee n reported in ClinVar (Variation ID: 156480). It has also been identified in 2/8 618 of East Asian chromosomes by the Exome Aggregation Consortium (ExAC, http:// exac.broadinstitute.org; dbSNP rs587783034). Computational prediction tools and conservation analysis do not provide strong support for or against an impact to the protein. In summary, the clinical significance of the p.Thr562Met variant is uncertain. |
Counsyl | RCV000144570 | SCV000785064 | uncertain significance | Familial adenomatous polyposis 1 | 2017-04-04 | criteria provided, single submitter | clinical testing | |
Myriad Genetics, |
RCV000144570 | SCV004018741 | likely benign | Familial adenomatous polyposis 1 | 2023-02-17 | criteria provided, single submitter | clinical testing | This variant is considered likely benign. This variant has been observed at a population frequency that is significantly greater than expected given the associated disease prevalence and penetrance. |
All of Us Research Program, |
RCV003998159 | SCV004837430 | uncertain significance | Classic or attenuated familial adenomatous polyposis | 2023-12-01 | criteria provided, single submitter | clinical testing | This missense variant replaces threonine with methionine at codon 562 of the APC protein. Computational prediction suggests that this variant may not impact protein structure and function (internally defined REVEL score threshold <= 0.5, PMID: 27666373). Splice site prediction tools suggest that this variant may not impact RNA splicing. To our knowledge, functional studies have not been performed for this variant. This variant has been reported in an individual affected with colorectal cancer (PMID: 28944238). This variant has been identified in 16/282672 chromosomes in the general population by the Genome Aggregation Database (gnomAD) and in healthy control individuals (PMID: 32980694). The available evidence is insufficient to determine the role of this variant in disease conclusively. Therefore, this variant is classified as a Variant of Uncertain Significance. |
Pathway Genomics | RCV000144570 | SCV000189866 | uncertain significance | Familial adenomatous polyposis 1 | 2014-07-24 | no assertion criteria provided | clinical testing |