Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV000235911 | SCV000293422 | pathogenic | not provided | 2016-01-13 | criteria provided, single submitter | clinical testing | This variant is denoted APC c.3306C>A at the cDNA level and p.Tyr1102Ter (Y1102X) at the protein level. The substitution creates a nonsense variant, which changes a Tyrosine to a premature stop codon (TAC>TAA), and is predicted to cause loss of normal protein function through protein truncation. Even though this frameshift occurs near the end of the gene in the last exon, and nonsense-mediated decay is not expected to occur, it is significant since the last 1741 amino acids are no longer translated. This variant has been reported in several individuals and families with Familial Adenomatous Polyposis (Miyaki 2008, Filipe 2009, Lagarde 2010) and is considered pathogenic. |
Myriad Genetics, |
RCV003337266 | SCV004044757 | pathogenic | Familial adenomatous polyposis 1 | 2023-05-08 | criteria provided, single submitter | clinical testing | This variant is considered pathogenic. This variant creates a termination codon and is predicted to result in premature protein truncation. |