Total submissions: 1
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
St. |
RCV002254860 | SCV002526043 | uncertain significance | Familial adenomatous polyposis 1 | 2022-05-02 | criteria provided, single submitter | clinical testing | The APC c.6627_6629del (p.Ser2210del) change results in the deletion of a single serine residue in exon 16 of the APC gene (BP3). This variant is absent in gnomAD v2.1.1 (PM2_supporting; https://gnomad.broadinstitute.org/). In silico analysis using PROVEAN predicts a benign effect of this variant on protein function (PMID: 23056405), but to our knowledge functional studies have not been performed. In summary, this variant meets criteria to be classified as of uncertain significance based on the ACMG/AMP criteria: PM2, BP3. |