Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV004565175 | SCV002290639 | uncertain significance | Familial adenomatous polyposis 1 | 2021-08-26 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002361381 | SCV002665155 | uncertain significance | Hereditary cancer-predisposing syndrome | 2020-12-08 | criteria provided, single submitter | clinical testing | The p.Q233P variant (also known as c.698A>C), located in coding exon 6 of the APC gene, results from an A to C substitution at nucleotide position 698. The glutamine at codon 233 is replaced by proline, an amino acid with similar properties. This amino acid position is highly conserved in available vertebrate species. In addition, in silico predictors for this gene do not accurately predict pathogenicity. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |