Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mayo Clinic Laboratories, |
RCV001508677 | SCV001714993 | uncertain significance | not provided | 2020-08-05 | criteria provided, single submitter | clinical testing | |
Fulgent Genetics, |
RCV002496420 | SCV002786531 | uncertain significance | Familial visceral amyloidosis, Ostertag type; Hypoalphalipoproteinemia, primary, 2; Hypoalphalipoproteinemia, primary, 2, intermediate | 2022-01-11 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV001508677 | SCV003440476 | uncertain significance | not provided | 2022-09-07 | criteria provided, single submitter | clinical testing | This variant is also known as APOA1 Baltimore and Arg10>Leu. In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Not Available"; PolyPhen-2: "Possibly Damaging"; Align-GVGD: "Not Available"). ClinVar contains an entry for this variant (Variation ID: 17920). This missense change has been observed in individual(s) with clinical features of APOA1-related conditions (PMID: 2108924). This variant is present in population databases (rs28929476, gnomAD 0.002%). This sequence change replaces arginine, which is basic and polar, with leucine, which is neutral and non-polar, at codon 34 of the APOA1 protein (p.Arg34Leu). |
OMIM | RCV000019513 | SCV000039810 | pathogenic | APOLIPOPROTEIN A-I (BALTIMORE) | 1990-04-01 | no assertion criteria provided | literature only |