Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Counsyl | RCV000665999 | SCV000790229 | uncertain significance | Arginase deficiency | 2017-03-08 | criteria provided, single submitter | clinical testing | |
Labcorp Genetics |
RCV000665999 | SCV001592148 | pathogenic | Arginase deficiency | 2020-08-07 | criteria provided, single submitter | clinical testing | This variant is not present in population databases (ExAC no frequency). For these reasons, this variant has been classified as Pathogenic. Algorithms developed to predict the effect of missense changes on protein structure and function are either unavailable or do not agree on the potential impact of this missense change (SIFT: "Deleterious"; PolyPhen-2: "Probably Damaging"; Align-GVGD: "Class C0"). This variant has been observed in individual(s) with arginase deficiency (PMID: 22959135, Invitae). It has also been observed to segregate with disease in related individuals. ClinVar contains an entry for this variant (Variation ID: 551041). This sequence change replaces glycine with aspartic acid at codon 27 of the ARG1 protein (p.Gly27Asp). The glycine residue is highly conserved and there is a moderate physicochemical difference between glycine and aspartic acid. |