Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Gene |
RCV001558303 | SCV001780217 | pathogenic | not provided | 2023-01-30 | criteria provided, single submitter | clinical testing | Frameshift variant predicted to result in protein truncation or nonsense mediated decay in a gene for which loss-of-function is a known mechanism of disease; Not observed at significant frequency in large population cohorts (gnomAD); Has not been previously published as pathogenic or benign to our knowledge; Truncating variants in this gene are considered pathogenic by a well-established clinical consortium and/or database |
Fulgent Genetics, |
RCV005040318 | SCV005681215 | likely pathogenic | Familial cancer of breast; Ataxia-telangiectasia syndrome | 2024-05-13 | criteria provided, single submitter | clinical testing |