Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
CHEO Genetics Diagnostic Laboratory, |
RCV003493312 | SCV004240436 | uncertain significance | Breast and/or ovarian cancer | 2023-04-26 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV004673902 | SCV005168090 | uncertain significance | Hereditary cancer-predisposing syndrome | 2024-04-11 | criteria provided, single submitter | clinical testing | The p.L804R variant (also known as c.2411T>G), located in coding exon 15 of the ATM gene, results from a T to G substitution at nucleotide position 2411. The leucine at codon 804 is replaced by arginine, an amino acid with dissimilar properties. This amino acid position is conserved. In addition, this alteration is predicted to be deleterious by in silico analysis. Based on the available evidence, the clinical significance of this variant remains unclear. |