Total submissions: 3
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Ambry Genetics | RCV000569340 | SCV000665236 | uncertain significance | Hereditary cancer-predisposing syndrome | 2023-05-26 | criteria provided, single submitter | clinical testing | The c.6199-5T>A intronic variant results from a T to A substitution 5 nucleotides upstream from coding exon 42 in the ATM gene. This nucleotide position is poorly conserved in available vertebrate species. In silico splice site analysis for this alteration is inconclusive and direct evidence is insufficient at this time (Ambry internal data). Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Labcorp Genetics |
RCV000697173 | SCV000825770 | likely benign | Ataxia-telangiectasia syndrome | 2024-07-01 | criteria provided, single submitter | clinical testing | |
Color Diagnostics, |
RCV000569340 | SCV000913093 | uncertain significance | Hereditary cancer-predisposing syndrome | 2018-12-10 | criteria provided, single submitter | clinical testing |