Total submissions: 4
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Labcorp Genetics |
RCV001372405 | SCV001569056 | uncertain significance | Ataxia-telangiectasia syndrome | 2023-06-19 | criteria provided, single submitter | clinical testing | In summary, the available evidence is currently insufficient to determine the role of this variant in disease. Therefore, it has been classified as a Variant of Uncertain Significance. An algorithm developed to predict the effect of missense changes on protein structure and function (PolyPhen-2) suggests that this variant is likely to be tolerated. ClinVar contains an entry for this variant (Variation ID: 1062663). This variant has not been reported in the literature in individuals affected with ATM-related conditions. This variant is not present in population databases (gnomAD no frequency). This sequence change replaces asparagine, which is neutral and polar, with serine, which is neutral and polar, at codon 272 of the ATM protein (p.Asn272Ser). |
Ambry Genetics | RCV002420840 | SCV002681770 | uncertain significance | Hereditary cancer-predisposing syndrome | 2021-07-23 | criteria provided, single submitter | clinical testing | The p.N272S variant (also known as c.815A>G), located in coding exon 6 of the ATM gene, results from an A to G substitution at nucleotide position 815. The asparagine at codon 272 is replaced by serine, an amino acid with highly similar properties. This alteration was observed with an allele frequency of 0.0000 in 7,051 unselected female breast cancer patients and was observed with an allele frequency of 0.00009 in 11,241 female controls of Japanese ancestry (Momozawa Y et al. Nat Commun, 2018 10;9:4083). This amino acid position is not well conserved in available vertebrate species. In addition, this alteration is predicted to be tolerated by in silico analysis. Since supporting evidence is limited at this time, the clinical significance of this alteration remains unclear. |
Baylor Genetics | RCV003469615 | SCV004212054 | uncertain significance | Familial cancer of breast | 2023-03-21 | criteria provided, single submitter | clinical testing | |
Natera, |
RCV001372405 | SCV002086013 | uncertain significance | Ataxia-telangiectasia syndrome | 2021-04-27 | no assertion criteria provided | clinical testing |