Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Research Unit for Rare Diseases, |
RCV001267645 | SCV001443817 | pathogenic | Wilson disease | criteria provided, single submitter | research | The NM_000053.4:c.3766C>T (p.Gln1256*) variant in ATP7B has been reported in one patient with Wilson disease in trans position with a variant NM_000053.4:c.2304dup (p.Met769fs). | |
Genome- |
RCV001267645 | SCV001977236 | pathogenic | Wilson disease | 2021-08-10 | criteria provided, single submitter | clinical testing |