Total submissions: 2
Submitter | RCV | SCV | Clinical significance | Condition | Last evaluated | Review status | Method | Comment |
---|---|---|---|---|---|---|---|---|
Mendelics | RCV000989387 | SCV001139701 | pathogenic | Bloom syndrome | 2019-05-28 | criteria provided, single submitter | clinical testing | |
Ambry Genetics | RCV002416269 | SCV002721720 | pathogenic | Hereditary cancer-predisposing syndrome | 2021-07-26 | criteria provided, single submitter | clinical testing | The p.R669* pathogenic mutation (also known as c.2005A>T), located in coding exon 7 of the BLM gene, results from an A to T substitution at nucleotide position 2005. This changes the amino acid from an arginine to a stop codon within coding exon 7. This variant is considered to be rare based on population cohorts in the Genome Aggregation Database (gnomAD). This alteration is expected to result in loss of function by premature protein truncation or nonsense-mediated mRNA decay. As such, this alteration is interpreted as a disease-causing mutation. |